First, do no harm: surgical management of von Hippel Lindau syndrome

Authors

  • Hannah Farley Oxford University

DOI:

https://doi.org/10.37707/jnds.v4i2.127

Keywords:

von hippel lindau, vhl, nephrectomy, partial nephrectomy, radical nephrectomy, bench surgery, renal autotransplant

Abstract

Von Hippel Lindau (VHL) syndrome is an inherited condition that is associated with retinal and central nervous system haemangioblastomas, as well as renal and pancreatic cysts (Varshney et al., 2017). The renal cysts have a significant likelihood of neoplastic change, and act as a pre-malignant pathological finding prior to the development of clear cell renal carcinoma.

Published

2023-08-06

Issue

Section

Case Studies